Keywords: Limit the type of heart disease
What is the limit type of heart disease
This disease mostly occurs in the tropical endocardial fibrosis (Endomyocardial Fibrosis) and occurs mostly in temperate eosinophil cardiomyopathy (Löffler s cardiomyopathy.), The disease is very rare in our country.
The cause is unknown, some people think that the Department of eosinophils increased degeneration caused autoimmune diseases.
Pathology and pathophysiology
The main lesion endocardial and endocardial fibrosis, myocardial thickening and endocardial thickening up to 10 times normal. Papillary muscles also atrophy, shortening, reduced ventricular chamber atrial enlargement. Intracardiac thrombosis. Fibrotic lesions often involving ventricular inflow tract atrioventricular valve regurgitation. Thickening and fibrosis of the endocardium and subendocardial lower compliance, diastolic and systolic function disorder. Diastolic ventricular diastolic restriction, increased atrial blood storage, atrial enlargement, hemodynamic changes similar constrictive pericarditis.
A common young adults, no significant gender differences, lesions may be confined to the left ventricle, right ventricle or biventricular simultaneously involved. As the lesion, and the different clinical manifestations.
First, the right ventricle lesions due to the slow onset of signs and symptoms, abdominal distension, ascites. Since the liver congestive hepatomegaly or ascites caused by abdominal wall stretching and abdominal pain. Of exertional dyspnea and paroxysmal nocturnal dyspnea, may paracentesis and alleviate the breathing difficulties are mainly caused by the ascites. Precordial discomfort, out of a sense of weakness output decreased, the labor force declined, half mild cough, expectoration. The main signs: the apex beat weaken, mild or moderate heart border to expand. The first heart sound weakened. The breastbone lower left edge of the hair of the systolic murmur. The third heart sound could be heard. Lower extremity edema and ascites disproportionate ascites volume and lower extremity edema lighter. With diuretics, lower extremity edema reduce or disappear, and ascites often persist jugular vein engorgement obvious.
Left ventricular lesions due to the signs and symptoms of palpitation, shortness of breath. Apical systolic murmur, hair-like minority apical systolic fine tremor. When the increase in pulmonary vascular resistance, the performance of pulmonary hypertension.
Biventricular lesions caused by the syndrome as the symptoms and signs of right ventricular and left ventricular endomyocardial fibrosis, but the signs and symptoms of right ventricular lesions mainly the outstanding performance of the small number of patients for cardiac arrhythmias, mostly for housing arrhythmias, which can lead to extreme expansion of the right atrium, or even collapse, death, and patients with chronic recurrent large pericardial effusion as the main performance, often mistaken for simple pericardial disease.
(A) X-ray examination of the enlargement of the heart, the right atrium or left atrial enlargement was significantly associated with pericardial effusion, heart shadow significantly increased, visible endocardium calcification.
(B) ECG the heart load increases, we can see the mitral P wave, atrial fibrillation, atrioventricular block and bundle branch block.
(C) cardiac catheterization right ventricular endomyocardial fibrosis, right ventricular compliance decreased right ventricular end-diastolic pressure increased was early diastolic subsidence, diastolic plateau wave. The right atrium and the superior vena cava pressure increased left ventricular endocardial fibrosis, pulmonary circulation pressure increases ventricular angiography shows reduced left ventricular cavity, blood flow is slow.
Diagnosis and differential diagnosis
The main manifestations of the disease, venous hypertension, jugular vein distention, hepatomegaly, ascites, lower extremity edema light and massive ascites. Spherical enlargement of the heart, the pulse weak, common atrioventricular valve regurgitation signs with cirrhosis of the liver, constrictive pericarditis, endocardial elastic fibers hyperplasia differentiated.
How to treat:
Avoid fatigue, prevent infection, heart failure can be used a strong heart, diuretic, vasodilator, but the effects are poor, and poor prognosis.
Second, the surgical treatment of endocardial dissection and valve replacement surgery, to good effect.